Department of Diagnostic Imaging, Pisa University Hospital, Pisa, Italy.
Hepatology Unit - Pisa University Hospital, Pisa, Italy.
J Med Imaging Radiat Oncol. 2021 Jun;65(3):323-330. doi: 10.1111/1754-9485.13173. Epub 2021 Mar 25.
Biliary hamartomas (BHs) are rare malformative cystic/cystic-like lesions of the liver affecting the biliary tree, named after Hanns von Meyenburg who described them for the first time and still known with this eponym to this day. They usually lack clinical symptoms, and abnormalities in liver function tests are unusual; thus, it is typically an incidental finding of liver imaging. Despite being benign lesions, BHs can pose clinical challenges; the first one is differential diagnosis with other more relevant pathological conditions. Therefore, knowledge of MR imaging findings of BHs is helpful for a prompt and correct diagnosis, avoiding unnecessary invasive procedures and/or an excessive number of radiological investigations. This pictorial review is aimed to depict the most typical MR imaging features of multiple biliary hamartomas (von Meyenburg Complex), in order to familiarize the diagnosis and facilitate the differentiation from other hepato-biliary cystic diseases.
胆管错构瘤(BHs)是一种罕见的肝脏胆管源性囊性/囊性样畸形病变,以首次描述它们的 Hanns von Meyenburg 的名字命名,至今仍以此命名。它们通常没有临床症状,肝功能试验异常也不常见;因此,它通常是肝脏影像学的偶然发现。尽管是良性病变,但 BHs 可能会带来临床挑战;第一个挑战是与其他更相关的病理情况进行鉴别诊断。因此,了解 BHs 的 MR 成像特征有助于快速准确地诊断,避免不必要的侵入性程序和/或过多的影像学检查。本影像学综述旨在描述多发性胆管错构瘤(von Meyenburg 复合体)的最典型 MR 成像特征,以便熟悉诊断并有助于与其他肝内胆管囊性疾病区分。