Jabarkhel Fatema, Puttonen Henri, Hansson Lina, Muth Andreas, Ragnarsson Oskar
Department of Internal Medicine and Clinical Nutrition, Institute of Medicine at Sahlgrenska Academy, University of Gothenburg and The Department of Endocrinology, Sahlgrenska University Hospital, Gothenburg, Sweden.
Department of Pathology, Sahlgrenska University Hospital, Gothenburg, Sweden.
J Endocr Soc. 2020 May 15;4(6):bvaa055. doi: 10.1210/jendso/bvaa055. eCollection 2020 Jun 1.
Primary adrenal leiomyosarcoma (PAL) is a rare, high-grade proliferating mesenchymal tumor with a considerable risk of metastasis, deriving from the smooth muscle wall of a central adrenal vein, or its tributaries. Roughly 40 patients with PAL have been reported in the literature. Herein, we present 3 patients with incidentally discovered PAL, along with an overview of the current knowledge on the clinical, radiological, and histopathological characteristics of PAL.
原发性肾上腺平滑肌肉瘤(PAL)是一种罕见的、高级别增殖性间叶肿瘤,转移风险相当高,起源于肾上腺中央静脉或其分支的平滑肌壁。文献中报道了约40例PAL患者。在此,我们报告3例偶然发现的PAL患者,并概述目前关于PAL临床、影像学和组织病理学特征的知识。