Laliotis Nikolaos A, Konstandinidis Panagiotis, Chrysanthou Chrysanthos K, Papadopoulou Lizeta
Department of Orthopaedics, Interbalkan Medical Center, Thessaloniki- 57001. Greece.
J Orthop Case Rep. 2019;9(5):7-10. doi: 10.13107/jocr.2019.v09.i05.1508.
Melorheostosis is a rare bone dysplasia. It is mainly a radiographic diagnosis with distinct findings of endosteal or periosteal sclerosis along the axis of long bones, resembling the flowing wax. It is usually polyostotic and monomelic. Clinical manifestations are pain, limitation of joint movements, deformities, and contractures. Leg length discrepancy may be found, usually the affected limb being shorter.
We present an adolescent boy, with melorheostosis of the lower limb. The affected limb was longer with equally divided discrepancy of the femur and tibia. There were no another symptoms. After a thorough investigation, we performed epiphysiodesis both medial and lateral of the distal femoral and proximal tibial growth plate, using8eight plates. At the end of the growth, there was almost complete equalization of the length of his lower limbs.
Melorheostosis may be present with leg length discrepancy leg length discrepancy, with an exception, being that the affected limb is longer. Epiphysiodesis with eight plates is an effective method of limb length equalization.
肢骨纹状肥大是一种罕见的骨发育异常。它主要是一种影像学诊断，具有沿长骨轴线的骨内膜或骨膜硬化的明显表现，类似流淌的蜡。它通常是多骨型且单肢型的。临床表现为疼痛、关节活动受限、畸形和挛缩。可能会发现下肢不等长，通常患侧肢体较短。
我们报告一名患有下肢肢骨纹状肥大的青少年男性。患侧肢体较长，股骨和胫骨的长度差异相等。无其他症状。经过全面检查后，我们使用8块钢板对股骨远端和胫骨近端生长板的内侧和外侧进行了骨骺阻滞术。在生长结束时，他的下肢长度几乎完全相等。
肢骨纹状肥大可能伴有下肢不等长，例外情况是患侧肢体较长。使用8块钢板进行骨骺阻滞术是肢体长度均衡的有效方法。
