Ku Min Jung, Kim Su Wan, Lee Seogjae, Chang Jee Won, Lee Jonggeun, Jeong Dong Seop
Department of Thoracic and Cardiovascular Surgery, Jeju National University Hospital, Jeju, Korea.
Department of Thoracic and Cardiovascular Surgery, Jeju National University School of Medicine, Jeju, Korea.
Korean J Thorac Cardiovasc Surg. 2020 Jun 5;53(3):140-143. doi: 10.5090/kjtcs.2020.53.3.140.
Primary cardiac sarcoma is rare, and intimal sarcoma is an extremely rare and highly lethal disease. We report a case of a 62-year-old woman who was incidentally diagnosed with a primary cardiac sarcoma originating from the left atrial appendage and extending to the left superior pulmonary vein. The location of the tumor was very complicated, posing a major challenge for complete resection. We successfully performed complete resection of the cardiac sarcoma via cardiac autotransplantation with left pneumonectomy. The patient recovered uneventfully, without any adjuvant therapy as of 6 months postoperatively. Autotransplantation of the heart may be suggested as a reasonable surgical option for extensive left atrial tumors.
原发性心脏肉瘤罕见,而内膜肉瘤是一种极其罕见且致死率很高的疾病。我们报告一例62岁女性病例,该患者偶然被诊断为起源于左心耳并延伸至左上肺静脉的原发性心脏肉瘤。肿瘤位置非常复杂,给完整切除带来了重大挑战。我们通过心脏自体移植联合左肺切除术成功地完整切除了心脏肉瘤。患者恢复顺利,术后6个月未接受任何辅助治疗。对于广泛累及左心房的肿瘤,心脏自体移植可能是一种合理的手术选择。