Honarmand Azim, Mirsatari Sayed Arash, Zarezadeh Abolghasem, Safavi Mohammadreza, Kheirabadi Dorna
Research Center of Anaesthesiology and Critical Care, Isfahan University of Medical Sciences, Isfahan, Iran.
Turk J Anaesthesiol Reanim. 2020 Jun;48(3):251-253. doi: 10.5152/TJAR.2020.93902. Epub 2020 Feb 5.
Werner syndrome (WS) is a rare hereditary disease, characterised by the clinical signs and symptoms of premature ageing. Patients with WS usually have difficult airway due to anatomic malformation of the oral cavity. General anaesthesia with endotracheal intubation poses a high risk for these patients. On the other hand, the risk associated with the peripheral nerve block is minimal. Here we report the successful management of a known case of WS by using a peripheral nerve block (axillary brachial plexus block) without any significant complications. The patient was a 39-year-old man, a known case of WS, admitted to the hospital with chief complaint of non-healing ulcers on his wrist and elbow due to the compression effect of the abnormal ulna bone on the overlying soft tissue. To the best of our knowledge, this is the first case report of using peripheral nerve block in the anaesthesia of a patient with WS.
沃纳综合征(WS)是一种罕见的遗传性疾病,其特征为过早衰老的临床体征和症状。WS患者通常因口腔解剖畸形而存在气道困难。气管插管全身麻醉对这些患者构成高风险。另一方面,周围神经阻滞相关风险极小。在此,我们报告了一例通过使用周围神经阻滞(腋路臂丛神经阻滞)成功管理已知WS病例的情况,且未出现任何严重并发症。该患者为一名39岁男性,已知患有WS,因异常尺骨对覆盖其上的软组织的压迫作用,以手腕和肘部溃疡不愈合为主诉入院。据我们所知,这是首例在WS患者麻醉中使用周围神经阻滞的病例报告。