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多模态影像学显示一种不常见的 pentad 中的心尖部肥厚型心肌病变异型。

Multimodality Imaging Demonstrating an Apical Variant Hypertrophic Cardiomyopathy in an Uncommon Pentad.

机构信息

Mayo Clinic Arizona, Phoenix, AZ, USA.

Tanta University, Tanta, Egypt.

出版信息

J Investig Med High Impact Case Rep. 2020 Jan-Dec;8:2324709620934324. doi: 10.1177/2324709620934324.

DOI:10.1177/2324709620934324
PMID:32551950
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC7303768/
Abstract

A 79-year-old man was admitted for a transcatheter aortic valve replacement due to severe aortic stenosis. A preoperative chest computed tomography with angiography revealed an apical variant hypertrophic cardiomyopathy with a prominent apical pouch. In addition, there was near-complete obliteration of the left ventricle in the mid to apical aspect during systole suggesting a midventricular gradient. Postoperative transthoracic echocardiography confirmed the apical variant hypertrophic cardiomyopathy with an apical aneurysm and a gradient with a peak velocity of 2 m/s, and mid-cavitary gradient with a peak velocity of 3 m/s. It also revealed a fusiform aneurysmal dilatation of the ascending aorta.

摘要

一位 79 岁男性因严重主动脉瓣狭窄接受经导管主动脉瓣置换术。术前胸部 CT 血管造影显示心尖部变异型肥厚型心肌病伴心尖部明显憩室。此外,收缩期中段至心尖部左心室几乎完全闭塞,提示中室间梯度。术后经胸超声心动图证实心尖部变异型肥厚型心肌病伴心尖部瘤和峰值速度为 2 m/s 的梯度,以及心腔中部峰值速度为 3 m/s 的梯度。还显示升主动脉梭形动脉瘤样扩张。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/025b/7303768/b727a03a7232/10.1177_2324709620934324-fig6.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/025b/7303768/20b03c7fc8ce/10.1177_2324709620934324-fig1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/025b/7303768/0dc1a0156557/10.1177_2324709620934324-fig2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/025b/7303768/ac72c6009cb6/10.1177_2324709620934324-fig3.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/025b/7303768/f36774ccd626/10.1177_2324709620934324-fig4.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/025b/7303768/a1095cfac73a/10.1177_2324709620934324-fig5.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/025b/7303768/b727a03a7232/10.1177_2324709620934324-fig6.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/025b/7303768/20b03c7fc8ce/10.1177_2324709620934324-fig1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/025b/7303768/0dc1a0156557/10.1177_2324709620934324-fig2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/025b/7303768/ac72c6009cb6/10.1177_2324709620934324-fig3.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/025b/7303768/f36774ccd626/10.1177_2324709620934324-fig4.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/025b/7303768/a1095cfac73a/10.1177_2324709620934324-fig5.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/025b/7303768/b727a03a7232/10.1177_2324709620934324-fig6.jpg

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