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肥厚型心肌病心尖部病变的演变:初诊11年后出现心室中部梗阻及心尖部室壁瘤。

The evolution of apical hypertrophic cardiomyopathy: Development of mid-ventricular obstruction and apical aneurysm 11 years after initial diagnosis.

作者信息

Singam Narayana Sarma V, Stoddard Marcus F

机构信息

Division of Cardiology, University of Louisville, Louisville, Kentucky.

出版信息

Echocardiography. 2019 May;36(5):987-991. doi: 10.1111/echo.14310. Epub 2019 Mar 13.

DOI:10.1111/echo.14310
PMID:30868653
Abstract

Asian hypertrophic cardiomyopathy (AHCM) is a rare variant of hypertrophic cardiomyopathy (HCM) that is more prevalent in the Asian population. There is significant overlap between AHCM, mid-cavitary obstruction, and apical aneurysms. Although more benign compared to HCM, the course of AHCM is not clearly defined. We present an interesting case of an African American male with known AHCM who develops symptomatic mid-cavitary obstruction and apical aneurysm 11 years after initial diagnosis.

摘要

亚洲肥厚型心肌病(AHCM)是肥厚型心肌病(HCM)的一种罕见变体,在亚洲人群中更为普遍。AHCM、心腔中部梗阻和心尖部动脉瘤之间存在显著重叠。尽管与HCM相比AHCM的病情相对较轻,但AHCM的病程尚不明确。我们报告了一例有趣的病例,一名已知患有AHCM的非裔美国男性,在初次诊断11年后出现有症状的心腔中部梗阻和心尖部动脉瘤。

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引用本文的文献

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Apical hypertrophic cardiomyopathy: pathophysiology, diagnosis and management.心尖肥厚型心肌病:病理生理学、诊断与治疗。
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