Department of Thoracic Surgery, Akashi Medical Center, 743-33 Okubocho Yagi, Akashi, Hyogo, 674-0063, Japan.
Division of Thoracic Surgery, Graduate School of Medicine, Kobe University, Kobe, Hyogo, 650-0017, Japan.
Gen Thorac Cardiovasc Surg. 2021 Jan;69(1):130-132. doi: 10.1007/s11748-020-01410-6. Epub 2020 Jun 18.
A 14-year-old girl was diagnosed with hemothorax associated with pulmonary arteriovenous fistula rupture, and emergency surgery was performed. One week before her surgery, her mother at 32 weeks of gestation underwent emergency surgery for hemothorax caused by pulmonary arteriovenous fistula rupture. Both were diagnosed with hereditary hemorrhagic telangiectasia. The indications for treatment of pulmonary arteriovenous fistulas in young patients remain controversial because the risk of complications concerning pulmonary arteriovenous fistula is lower in young patients than in adult patients. We recommend that aggressive treatment should be performed for pulmonary arteriovenous fistulas in patients with hereditary hemorrhagic telangiectasis with a family history of pulmonary arteriovenous fistula rupture even if the patient is asymptomatic and young, because such patients may have a high risk of pulmonary arteriovenous fistula rupture.
一位 14 岁女孩被诊断为与肺动静脉瘘破裂相关的血胸，并进行了紧急手术。在她手术前一周，她的母亲在妊娠 32 周时因肺动静脉瘘破裂引起的血胸接受了紧急手术。两人均被诊断为遗传性出血性毛细血管扩张症。年轻患者肺动静脉瘘的治疗指征仍存在争议，因为年轻患者肺动静脉瘘并发症的风险低于成年患者。我们建议对于有肺动静脉瘘破裂家族史的遗传性出血性毛细血管扩张症患者，即使患者无症状且年轻，也应积极治疗肺动静脉瘘，因为此类患者肺动静脉瘘破裂的风险可能较高。
