Department of Pediatric Surgery, Leipzig University, Leipzig, Sachsen, Germany.
Department of Medical Psychology, University Medical Center, Hamburg, Eppendorf, Germany.
Eur J Pediatr Surg. 2020 Jun;30(3):279-286. doi: 10.1055/s-0040-1713597. Epub 2020 Jun 26.
Anorectal malformation (ARM) and Hirschsprung's disease (HD) are the most common congenital colorectal anomalies. Despite advances in surgical techniques and improvements in postoperative clinical care, short- and long-term physical and psychosocial morbidity of these patients remains high. This review outlines the current literature on the physical and psychosocial aspects of health-related quality of life (HrQoL) and its confounders in patients with ARM/HD. Moreover, important coping strategies are summarized to further improve HrQoL of ARM/HD patients and their families.
肛门直肠畸形（ARM）和先天性巨结肠（HD）是最常见的先天性结直肠畸形。尽管手术技术不断进步，术后临床护理也有所改善，但这些患者的短期和长期身体和心理社会发病率仍然很高。本文综述了有关 ARM/HD 患者健康相关生活质量（HrQoL）及其混杂因素的当前文献，并总结了重要的应对策略，以进一步提高 ARM/HD 患者及其家属的 HrQoL。
