一种不同类型的狼：首例已知的伴有三度房室传导阻滞需植入起搏器的Wolf-Hirschhorn综合征病例。
A Different Breed of Wolf: First Known Case of Wolf-Hirschorn Syndrome with Third-degree Atrioventricular Block Requiring Pacemaker Implantation.
作者信息
Percell Robert Lee, Percell Hyacinth C, Miller Keith A
机构信息
Electrophysiology Section, Bryan Heart Institute, Lincoln, NE, USA.
出版信息
J Innov Card Rhythm Manag. 2020 Jun 15;11(6):4147-4150. doi: 10.19102/icrm.2020.110601. eCollection 2020 Jun.
Abstract
We describe a case of a 44-year-old male with a history of Wolf-Hirschorn syndrome (WHS) with seizures and mental retardation who was evaluated for what was thought to be a seizure. He was found to be severely bradycardic with a heart rate of 24 bpm. The electrocardiogram revealed third-degree atrioventricular block and he subsequently underwent an uncomplicated single-chamber pacemaker implantation procedure. This is a unique report given its status as the first described case of bradycardic rhythm abnormalities in a patient with WHS.
摘要
我们描述了一例44岁男性患者，有Wolf-Hirschorn综合征（WHS）病史，伴有癫痫发作和智力发育迟缓，此次因疑似癫痫发作接受评估。发现他严重心动过缓，心率为24次/分钟。心电图显示三度房室传导阻滞，随后他接受了一次简单的单腔起搏器植入手术。鉴于这是首次报道的WHS患者出现心动过缓节律异常的病例，此报告具有独特性。
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