Lasam Glenmore, Lasam Marcelina
Morristown Medical Center, Morristown, NJ 07960, USA.
Overlook Medical Center, Summit, NJ 07901, USA.
Cardiol Res. 2018 Jun;9(3):176-179. doi: 10.14740/cr673w. Epub 2018 Jun 6.
A case of a 73-year-old woman with a history of von Recklinghausen disease (neurofibromatosis type 1) who presented initially with a gradual onset of shortness of breath and lightheadedness with no associated fever, chills, angina, palpitations, cough, weight loss, night sweats, nausea, vomiting, or constipation. She was found to be severely bradycardic and in third degree atrioventricular block by her primary care physician. She was admitted in the hospital because of intermittent bouts of lightheadedness and progression of the shortness of breath. Twelve-lead electrocardiogram documented the high grade atrioventricular block. Chest radiograph showed subtle mild pulmonary congestion. Transthoracic echocardiogram revealed mild concentric hypertrophy and normal systolic function with no regional wall motion abnormalities or evidence of significant valvular disease. Pacemaker was inserted and her symptoms improved significantly.
一名73岁女性，有冯雷克林霍增氏病（1型神经纤维瘤病）病史，最初表现为逐渐出现的呼吸急促和头晕，无发热、寒战、心绞痛、心悸、咳嗽、体重减轻、盗汗、恶心、呕吐或便秘。她的初级保健医生发现她严重心动过缓，存在三度房室传导阻滞。由于间歇性头晕和呼吸急促加重，她入院治疗。十二导联心电图记录了高度房室传导阻滞。胸部X光片显示有轻微的肺部充血。经胸超声心动图显示轻度向心性肥厚，收缩功能正常，无节段性室壁运动异常或明显瓣膜疾病的证据。植入了起搏器，她的症状明显改善。
