Sonu Sumit Kumar, Lai Yi Wye, Verma Kamal, Sitoh Yih Yian, Purohit Bela
Dept. of Neurology, National Neuroscience Institute, 11 Jln Tan Tock Seng, 308433, Singapore.
Dept. of Internal medicine, Tan Tock Seng Hospital, 11 Jln Tan Tock Seng, 308433, Singapore.
Radiol Case Rep. 2020 Jun 23;15(8):1323-1330. doi: 10.1016/j.radcr.2020.05.062. eCollection 2020 Aug.
Rhombencephalitis (RE) refers to inflammatory diseases involving the brainstem and cerebellum. Although RE is a rare entity, it is associated with high morbidity and mortality. The management of such patients is often challenging in terms of identifying the etiology and defining prognosis. Infections, autoimmune and paraneoplastic conditions are commonly implicated. Patients with RE often present with a biphasic illness with an initial flu-like syndrome followed by brainstem dysfunction. CSF pleocytosis, abnormal brain MRI findings, isolation of organism or molecular (PCR/antigen) detection in CSF/blood cultures/stool samples and nasal/rectal swabs help in arriving at a definitive or probable diagnosis. Prompt aggressive treatment with antibacterial and antiviral drugs and/or immunoglobulins along with supportive therapy is crucial for avoiding a poor outcome. We present a case report of a 28-year old female patient who developed RE and myelitis in the third trimester of pregnancy. We aim to highlight the highly suggestive radiological findings which corroborated with the clinical diagnosis of enterovirus infection. The patient's radiological follow-up and neurological sequalae are also described. To the best of our knowledge, ours is the first report which describes the MRI features of this clinical scenario in the third trimester of pregnancy, and also the subsequent clinico-radiological follow up.
菱脑炎(RE)是指累及脑干和小脑的炎症性疾病。尽管RE是一种罕见疾病,但它与高发病率和高死亡率相关。在确定病因和判断预后方面,对此类患者的治疗往往具有挑战性。感染、自身免疫性和副肿瘤性疾病通常与之相关。RE患者常表现为双相性疾病,初期有类似流感的综合征,随后出现脑干功能障碍。脑脊液细胞增多、脑部MRI检查结果异常、在脑脊液/血培养/粪便样本以及鼻拭子/直肠拭子中分离出病原体或进行分子(PCR/抗原)检测有助于做出明确或可能的诊断。及时使用抗菌和抗病毒药物及/或免疫球蛋白进行积极治疗并辅以支持治疗对于避免不良预后至关重要。我们报告一例28岁女性患者,在妊娠晚期发生了RE和脊髓炎。我们旨在强调高度提示性的影像学表现,这些表现与肠道病毒感染的临床诊断相符。还描述了该患者的影像学随访情况及神经后遗症。据我们所知,我们的报告是首例描述妊娠晚期这种临床情况的MRI特征以及后续临床影像学随访的报告。