Department of Thoracic and Cardiovascular Surgery, St. Vincent's Hospital, College of Medicine, The Catholic University of Korea, Suwon, Republic of Korea.
Department of Thoracic and Cardiovascular Surgery, Sejong General Hospital, Sejong Heart Institute, 28, Hohyeon-ro 489 Beon-gil, Sosa-gu, Bucheon, Gyeonggi-do, 422-711, Republic of Korea.
Pediatr Cardiol. 2020 Oct;41(7):1501-1508. doi: 10.1007/s00246-020-02394-z. Epub 2020 Jul 29.
Aortic root dilatation is frequently encountered in adults with repaired Tetralogy of Fallot (TOF). The timing of total repair is known to have a significant correlation with late aortic root dilatation, but it is not well established. The objective of this study was to investigate the risk factors and correlation with timing of total repair for aortic root dilatation in adults with repaired TOF. An observational retrospective cohort study was conducted in 314 adults (≥ 18 years) with repaired TOF. Aortic root dilatation was defined when the absolute diameter of Sinus of Valsalva (SoV) was over 40 mm. SoV was measured by echocardiography in 110 patients, computed tomography angiography in 168 patients, and magnetic resonance image in 36 patients. Aortic root dilatation was observed in 65 patients (20.7%). Among them, 3 patients underwent Bentall operation due to acute aortic dissection or aortic root aneurysm. On multivariate logistic regression analysis, age at total repair was a significant risk factor for late aortic root dilatation (OR = 3.14; 95% CI 1.62-6.08; p = 0.001) and the cutoff value of age was 1.9 years. However, late aortic root dilatation was also observed in 10% of patients (10/91) who operated before 1 year of age. Late total repair was a significant risk factor for late aortic root dilatation in repaired TOF. However, early total repair did not always prevent late aortic root dilatation. These results suggest that congenital aortic pathology may also be a possible cause of aortic root dilatation along with longstanding hemodynamic stress.
主动脉根部扩张在修复法洛四联症(TOF)的成年患者中经常遇到。众所周知,总修复的时机与晚期主动脉根部扩张有显著相关性,但尚未得到充分证实。本研究旨在探讨修复 TOF 成人主动脉根部扩张的危险因素及其与总修复时机的相关性。
一项观察性回顾性队列研究纳入了 314 名(≥18 岁)修复 TOF 的成年患者。当窦部(SoV)绝对直径超过 40mm 时,定义为主动脉根部扩张。通过超声心动图测量了 110 例患者的 SoV,通过计算机断层扫描血管造影术测量了 168 例患者的 SoV,通过磁共振成像测量了 36 例患者的 SoV。65 例患者(20.7%)观察到主动脉根部扩张。其中,3 例因急性主动脉夹层或主动脉根部动脉瘤而行 Bentall 手术。
多变量逻辑回归分析显示,总修复时的年龄是晚期主动脉根部扩张的显著危险因素(OR=3.14;95%CI 1.62-6.08;p=0.001),年龄的截断值为 1.9 岁。然而,10%(10/91)的 1 岁以内手术患者也发生了晚期主动脉根部扩张。
晚期总修复是修复 TOF 患者晚期主动脉根部扩张的显著危险因素。然而,早期总修复并不总是能预防晚期主动脉根部扩张。这些结果表明,先天性主动脉病变也可能是导致主动脉根部扩张的一个原因,同时还有长期血流动力学压力的作用。