Oh Moon Young, Kim Hyo Kee, Han Ahram, Yi Nam-Joon, Min Seung-Kee
Department of Surgery, Seoul National University Hospital, Seoul, Korea.
Division of Vascular Surgery, Department of Surgery, Seoul National University College of Medicine, Seoul, Korea.
Vasc Specialist Int. 2020 Sep 30;36(3):186-192. doi: 10.5758/vsi.200018.
Extrahepatic portal vein obstruction (EHPVO) is the most common cause of pediatric portal hypertension and can cause life-threatening variceal bleeding. Meso- Rex shunt (MRS) is a surgical procedure that restores physiological portal venous blood flow to the liver by using a graft to connect the superior mesenteric vein and the left portal vein within the Rex recess, and can relieve variceal bleeding and other complications associated with EHPVO. Although the MRS is regarded as an optimal and potentially curative treatment with good long-term patency, graft thrombosis or failure due to unknown causes is not rare, prompting the need for further research on the risk factors of graft failure or poor patency. Herein, we report two cases of EHPVO in patients with recurrent or uncontrolled variceal bleeding, one treated with the classic Rex shunt and the other with the modified Rex shunt, which resulted in a failure and success, respectively.
肝外门静脉阻塞(EHPVO)是儿童门静脉高压最常见的原因,可导致危及生命的静脉曲张出血。肠系膜上静脉-门静脉左支分流术(MRS)是一种外科手术,通过使用移植物在雷克斯隐窝内连接肠系膜上静脉和门静脉左支,恢复肝脏的生理性门静脉血流,并可缓解与EHPVO相关的静脉曲张出血和其他并发症。尽管MRS被认为是一种具有良好长期通畅性的最佳且可能治愈的治疗方法,但由于不明原因导致的移植物血栓形成或失败并不罕见,这促使人们需要进一步研究移植物失败或通畅性差的危险因素。在此,我们报告两例复发性或无法控制的静脉曲张出血患者的EHPVO病例,一例采用经典雷克斯分流术治疗,另一例采用改良雷克斯分流术治疗,结果分别为失败和成功。