Guzik Paul, Han Audrey, Shapiro Samantha C, Shaikh Kamran
UNIVERSITY OF TEXAS AT AUSTIN DELL MEDICAL SCHOOL, AUSTIN, TEXAS.
Methodist Debakey Cardiovasc J. 2020 Apr-Jun;16(2):162-166. doi: 10.14797/mdcj-16-2-162.
Cardiac involvement of infiltrative disease, such as systemic sclerosis, carries significant morbidity and mortality. All parts of the heart may be affected, although the conduction system is less commonly involved. We report a rare case of systemic sclerosis causing third-degree atrioventricular block and the first known reported case to use cardiac magnetic resonance imaging (CMR) as a diagnostic and prognostic instrument. It is not known whether using cardiac CMR in systemic sclerosis with cardiac involvement could lead to earlier intervention with escalation of medical therapy or earlier referral for transplant evaluation.
浸润性疾病累及心脏，如系统性硬化症，会带来显著的发病率和死亡率。心脏的所有部位都可能受到影响，尽管传导系统较少受累。我们报告了一例罕见的系统性硬化症导致三度房室传导阻滞的病例，这也是首例已知使用心脏磁共振成像（CMR）作为诊断和预后评估工具的病例。目前尚不清楚，在心脏受累的系统性硬化症患者中使用心脏CMR是否能促使更早地进行强化药物治疗干预或更早地转诊进行移植评估。
