Leung Almond, Elasir Haitham M, Mahawish Karim M
geriatric and stroke medicine, MidCentral DHB, Palmerston North, New Zealand.
MidCentral DHB, Palmerston North, New Zealand.
Clin Med (Lond). 2020 Jul;20(4):440-441. doi: 10.7861/clinmed.2020-0288.
Idiopathic retroperitoneal fibrosis is a rare disease. Symptoms include constitutional symptoms and abdominal/flank pain. Causes of retroperitoneal fibrosis include non-infectious and infectious etiologies. Of the infectious etiologies, tuberculous aortitis is an important differential as it is associated with a high mortality rate. We present a case of a 59-year-old man with a retroperitoneal periaortic mass initially diagnosed as tuberculous aortitis. However following biopsy, the diagnosis was later amended to idiopathic retroperitoneal fibrosis with latent tuberculosis. He was successfully treated with prednisone and methotrexate.
特发性腹膜后纤维化是一种罕见疾病。症状包括全身症状和腹部/侧腹痛。腹膜后纤维化的病因包括非感染性和感染性病因。在感染性病因中,结核性主动脉炎是一个重要的鉴别诊断,因为它与高死亡率相关。我们报告一例59岁男性,其腹膜后主动脉周围肿块最初被诊断为结核性主动脉炎。然而,活检后诊断改为特发性腹膜后纤维化合并潜伏性结核。他接受泼尼松和甲氨蝶呤治疗后获得成功。