Bhushan Shreya, Goyal Vikas, Ward Cameron, Rashid Muddassir, Kapur Nitin
Department of Respiratory and Sleep Medicine Queensland Children's Hospital Brisbane QLD Australia.
Department of Cardiology Queensland Children's Hospital Brisbane QLD Australia.
Respirol Case Rep. 2020 Jul 16;8(7):e00620. doi: 10.1002/rcr2.620. eCollection 2020 Oct.
Tracheal and bronchial varices are rarely found in children. However, they have been described in adults with failing Fontan circuits or secondary to vascular pathology, such as portal and pulmonary hypertension. We report the presentation of haemoptysis and bronchial varices in a child, six years after a Fontan procedure for tricuspid atresia. She had tortuous mediastinal and transpleural arterial collaterals on computed tomography (CT) angiography and cardiac catheterization and subsequently underwent embolization of these collaterals. While the haemoptysis settled post embolization, the bronchial varices persisted on repeat bronchoscopy. She has since been clinically well with no further haemoptysis.
气管和支气管静脉曲张在儿童中很少见。然而，在患有功能性Fontan循环衰竭的成人或继发于血管病变（如门静脉高压和肺动脉高压）的成人中已有相关描述。我们报告了一名儿童在接受三尖瓣闭锁Fontan手术后六年出现咯血和支气管静脉曲张的情况。她在计算机断层扫描（CT）血管造影和心脏导管检查中发现有迂曲的纵隔和经胸膜动脉侧支，随后对这些侧支进行了栓塞治疗。虽然咯血在栓塞后得到缓解，但重复支气管镜检查时支气管静脉曲张仍然存在。此后她临床状况良好，未再出现咯血。
