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一名青少年的肺胸膜母细胞瘤。

Pleuropulmonary blastoma in an adolescent.

作者信息

Bownes Laura V, Hutchins Sara C, Cardenas Agustin M, Kelly David R, Beierle Elizabeth A

机构信息

Division of Pediatric Surgery, Department of Surgery, University of Alabama, Birmingham, Birmingham, AL, USA.

Division of Hematology and Oncology, Department of Medicine, University of Alabama, Birmingham, Birmingham, AL, USA.

出版信息

J Pediatr Surg Case Rep. 2020 Aug;59. doi: 10.1016/j.epsc.2020.101482. Epub 2020 May 23.

DOI:10.1016/j.epsc.2020.101482
PMID:32699772
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC7375461/
Abstract

Primary pulmonary malignancies are rare in childhood. The most common, pleuropulmonary blastoma (PPB), has an incidence of 25-50 cases per year in the United States (Knight and et al., 2019) [1]. The majority of children are diagnosed with PPB before the age of four years. PPB is divided into subtypes I, Ir (type I-regressed), II, and III, which correlates to the age of diagnosis and patient prognosis [2,3]. Here we report an unusual presentation of PPB in a teen-aged female who presented with a one month history of a non-productive cough.

摘要

原发性肺恶性肿瘤在儿童时期较为罕见。最常见的是胸膜肺母细胞瘤(PPB),在美国每年的发病率为25 - 50例(奈特等人,2019年)[1]。大多数儿童在4岁之前被诊断出患有PPB。PPB分为I型、Ir(I型消退型)、II型和III型,这与诊断年龄和患者预后相关[2,3]。在此,我们报告一名青少年女性PPB的不寻常表现,该患者有1个月干咳病史。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/edbe/7375461/4dbd074737c4/nihms-1608875-f0003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/edbe/7375461/5d10ebe9c7fd/nihms-1608875-f0001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/edbe/7375461/6988acf7b4f8/nihms-1608875-f0002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/edbe/7375461/4dbd074737c4/nihms-1608875-f0003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/edbe/7375461/5d10ebe9c7fd/nihms-1608875-f0001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/edbe/7375461/6988acf7b4f8/nihms-1608875-f0002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/edbe/7375461/4dbd074737c4/nihms-1608875-f0003.jpg

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本文引用的文献

1
Pleuropulmonary Blastoma: More Than a Lung Neoplasm of Childhood.胸膜肺母细胞瘤:不仅仅是一种儿童肺部肿瘤。
Mo Med. 2019 May-Jun;116(3):206-210.
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Current Management of Pleuropulmonary Blastoma: A Surgical Perspective.肺胚细胞瘤的当前管理:外科视角
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Metachronous pleuropulmonary blastoma in an adult patient with endometrial cancer: a case report.
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Unusual thoracic tumor in a teenager: A rare occurrence.青少年中的罕见胸段肿瘤:一例罕见病例。
Qatar Med J. 2022 Mar 1;2022(1):12. doi: 10.5339/qmj.2022.12. eCollection 2022.
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Type II pleuropulmonary blastoma in a 3-years-old female with dyspnea: a case report and review of literature.一名3岁呼吸困难女童的II型胸膜肺母细胞瘤:病例报告及文献复习
Radiol Case Rep. 2021 Jul 18;16(9):2736-2741. doi: 10.1016/j.radcr.2021.06.022. eCollection 2021 Sep.
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A Case Report of Pleuropulmonary Blastoma Presenting as Tension Pneumothorax.
Indian J Med Paediatr Oncol. 2017 Jan-Mar;38(1):70-72. doi: 10.4103/0971-5851.203515.
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Pleuropulmonary blastoma: a report on 350 central pathology-confirmed pleuropulmonary blastoma cases by the International Pleuropulmonary Blastoma Registry.胸膜肺母细胞瘤:国际胸膜肺母细胞瘤登记处关于350例经中心病理确诊的胸膜肺母细胞瘤病例的报告。
Cancer. 2015 Jan 15;121(2):276-85. doi: 10.1002/cncr.29032. Epub 2014 Sep 10.
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