Addanki Archana, Chaitanya Krishna, Bartakke Sandip, Sethuratnam Srividya
Department of Pediatric Hemato-oncology, Aditya Birla Memorial Hospital, Pune, Maharashtra, India.
Indian J Med Paediatr Oncol. 2017 Jan-Mar;38(1):70-72. doi: 10.4103/0971-5851.203515.
Pleuropulmonary blastoma (PPB) is a very rare, highly aggressive, and malignant tumor that originates from either lungs or pleura. It occurs mainly in children aged <5 or 6 years. It has poor prognosis with three different subtypes: cystic (type I), combined cystic and solid (type II), and solid (type III). PPB is treated with aggressive multimodal therapies including surgery and chemotherapy. We present a case of PPB in a 3-year-old girl who presented with tension pneumothorax.