Division of Cardiology, 1st Department of Internal Medicine, University of Pécs Medical School, Ifjúság Street 13, Pécs, 7624, Hungary.
Division of Heart Surgery, 2nd Department of Internal Medicine and Cardiology Center, Albert Szent-Györgyi Health Center, University of Szeged Faculty of Medicine, Szeged, Hungary.
ESC Heart Fail. 2020 Oct;7(5):3203-3207. doi: 10.1002/ehf2.12913. Epub 2020 Jul 23.
Coronary artery fistula is a rare congenital cardiac anomaly that is often found incidentally during computed tomography angiography. Coronary fistula between the left circumflex coronary artery and the coronary sinus is among the less common forms of coronary artery fistula. A 60-yea\r-old female patient presented to our outpatient cardiology department with symptoms of severe, de novo heart failure. Echocardiogram revealed severe mitral regurgitation and a dilated duct that turbulently accelerated colour Doppler flow behind the left ventricle with significant left-to-right shunt. Cardiac magnetic resonance imaging and computed tomography angiography revealed a massively dilated fistula between the left circumflex coronary artery and the coronary sinus with a diameter of 3-4 cm. The patient underwent combined heart surgery involving mitral ring annuloplasty and fistula ligation and was discharged in stable condition on guideline-based medical therapy. At 18 months of follow-up, minimal residual shunt flow and mild-to-moderate mitral regurgitation were found. We report a rare case of congenital coronary disorder resulting in heart failure and highlight the importance of complex non-invasive cardiac diagnostic procedures before planning and performing heart surgery.
冠状动脉瘘是一种罕见的先天性心脏畸形,通常在计算机断层血管造影检查中偶然发现。左回旋支冠状动脉和冠状窦之间的冠状动脉瘘是较少见的冠状动脉瘘形式之一。一名 60 岁女性患者因严重新发心力衰竭到我院心内科门诊就诊。超声心动图显示严重二尖瓣反流和扩张的导管,在左心室后面湍流加速彩色多普勒血流,存在明显的左向右分流。心脏磁共振成像和计算机断层血管造影显示左回旋支冠状动脉和冠状窦之间有一个直径为 3-4 厘米的巨大扩张瘘。患者接受了联合心脏手术,包括二尖瓣环成形术和瘘结扎术,并在基于指南的药物治疗下稳定出院。在 18 个月的随访中,发现残余分流流量较小,二尖瓣反流轻度至中度。我们报告了一例罕见的先天性冠状动脉疾病导致心力衰竭的病例,并强调在计划和进行心脏手术之前,进行复杂的非侵入性心脏诊断程序的重要性。