Mahajan Sachin, Khanna Sudhansoo, Rohit Manojkumar, Chakraborty Nirupam S, Singhal Ankit
Department of Cardiovascular and Thoracic Surgery, Post Graduate Institute of Medical Education and Research (PGIMER), Chandigarh, India.
Department of Cardiology, Post Graduate Institute of Medical Education and Research (PGIMER), Chandigarh, India.
J Card Surg. 2020 Sep;35(9):2399-2402. doi: 10.1111/jocs.14792. Epub 2020 Jul 27.
Congenital superior vena cava (SVC) stenosis is a very rare anomaly, especially in pediatric population. Coexistence with obstructed supracardiac total anomalous pulmonary venous connection (TAPVC) has never been reported. Clinical examination should prompt detailed and focused evaluation for this treatable etiology. Pericardial patch augmentation can cure SVC stenosis, and may allow for growth potential as well. We describe a case of congenital SVC stenosis in a case of obstructed supracardiac TAPVC in a 3-month-old infant, managed successfully.
先天性上腔静脉(SVC)狭窄是一种非常罕见的异常情况,尤其是在儿科人群中。与梗阻性心上型完全性肺静脉异位连接(TAPVC)并存的情况从未有过报道。临床检查应促使对这种可治疗病因进行详细且有针对性的评估。心包补片扩大术可治愈SVC狭窄,并且可能也保留了生长潜力。我们描述了一例3个月大婴儿患有梗阻性心上型TAPVC合并先天性SVC狭窄的病例,该病例得到了成功治疗。