Matsuwaka R, Tomokuni T, Ishikawa S, Watanabe F, Matsushita T, Matsuda H
Division of Cardiovascular Surgery, Osaka University Medical School, Japan.
Eur J Cardiothorac Surg. 1987;1(3):180-2. doi: 10.1016/1010-7940(87)90038-8.
A case of tricuspid atresia associated with partially unroofed coronary sinus following a Fontan operation is described. A 4-year-old boy with tricuspid atresia showed persistent arterial desaturation immediately after a modified Fontan operation. At reoperation on the next day, a partially unroofed coronary sinus was recognized and repaired through a left atriotomy. Although uncommon, this associated anomaly should be kept in mind even in the absence of a persistent left superior vena cava and should be suspected if arterial desaturation occurs after a modified Fontan operation.
本文描述了一例在Fontan手术后出现三尖瓣闭锁合并部分性冠状静脉窦顶缺如的病例。一名患有三尖瓣闭锁的4岁男孩在改良Fontan手术后立即出现持续性动脉血氧饱和度降低。在术后第二天再次手术时，发现了部分性冠状静脉窦顶缺如，并通过左心房切开术进行了修复。尽管这种相关异常并不常见，但即使在没有持续性左上腔静脉的情况下也应予以考虑，如果在改良Fontan手术后出现动脉血氧饱和度降低，就应怀疑有这种情况。
