Department of Pediatric Surgery, 16512Hospital Sant Joan de Déu, University of Barcelona, Spain.
Department of Pediatric Surgery, 156300Hospital Universitario de Burgos, Spain.
Cleft Palate Craniofac J. 2020 Dec;57(12):1422-1427. doi: 10.1177/1055665620947957. Epub 2020 Aug 18.
Congenital midline cervical cleft is a rare malformation. Typical case shows an area of hypotrophic skin, a cranial nipple-like structure, and a caudal blind sinus. Cervical extension is limited. Relapse of the retraction is common following cutaneous z-plasty. The aim of this study is to describe the radiological, surgical, and histological findings of the 4 cases treated in our center in the last 8 years and communicate the finding of a contractile structure, anterior to the platysma, composed by striated muscle, figure not previously described. This distinct muscular band is responsible for neck retraction. Removal of this releases cervical tension and is essential to avoid the relapse.
先天性中线颈裂是一种罕见的畸形。典型病例表现为一局限性皮肤发育不良区,类似颅顶乳头样结构,以及尾端盲窦。颈部伸展受限。行皮瓣成形术后,回缩常复发。本研究旨在描述 8 年来在我中心治疗的 4 例患者的放射学、手术和组织学表现,并报告一种以前未描述的位于颈阔肌前方的收缩性结构的发现,该结构由横纹肌组成。这条明显的肌肉束是导致颈部回缩的原因。切除该肌肉束可释放颈部张力,对于避免复发至关重要。