肿瘤性硬化性黏液水肿一例罕见病例。

A Rare Case of Tumoral Scleromyxedema.

作者信息

Sadeghinia Ali, Al Salman Mohammad, Fazli Jafar Taghizadeh, Normohammadpour Pedram, Ehsani Amir Hooshang, Emadi Seyed Naser

机构信息

Department of Dermatology, Razi Hospital, Tehran University of Medical Sciences, Tehran, Iran.

出版信息

Indian J Dermatol. 2020 Jul-Aug;65(4):310-312. doi: 10.4103/ijd.IJD_450_18.

DOI:10.4103/ijd.IJD_450_18

PMID:32831375

原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC7423223/

Abstract

Scleromyxedema is an uncommon disease, affecting the skin mainly and other internal organs sometimes, characterized by fibroblasts proliferation, fibrosis, and mucous deposition in the absence of thyroid disorder. It is associated with monoclonal gammopathy in most cases. We are reporting a case with a rare presentation of tumoral scleromyxedema in the neck, with a mass mimicking other tumoral lesions, highlighting the importance of diagnosis and histopathologic correlation.

摘要

硬化性黏液水肿是一种罕见疾病，主要累及皮肤，有时也影响其他内脏器官，其特征为成纤维细胞增殖、纤维化及黏液沉积，且无甲状腺疾病。大多数情况下，它与单克隆丙种球蛋白病相关。我们报告一例颈部肿瘤性硬化性黏液水肿的罕见病例，其肿块类似其他肿瘤性病变，强调了诊断及组织病理学关联的重要性。