BaŞ İkİzoĞlu Nilay, AtaĞ Emine, Ergenekon Almala Pınar, Yilmaz YeĞİt Cansu, GÖkdemİr Yasemin, Erdem Eralp Ela, BÜge Öz Ayşim, Karadag Bulent
Department of Pediatrics, Division of Pediatric Pulmonology, Marmara University School of Medicine, Istanbul, Turkey.
Department of Pathology, Istanbul University Cerrahpaşa Faculty of Medicine, Istanbul, Turkey.
Arch Rheumatol. 2019 Oct 16;35(2):283-286. doi: 10.46497/ArchRheumatol.2020.7459. eCollection 2020 Jun.
Behçet's disease (BD) is a rare autoimmune and chronic inflammatory vasculitis, characterized by relapsing episodes of oral aphthous and genital ulcers, skin lesions, ocular lesions and vascular involvement. Pulmonary artery involvement is rare in BD but it carries a high mortality risk. In this article, we report a 15-year-old male patient presented with a two-month history of hemoptysis, cough, fewer and weight loss. On physical examination, auscultation revealed decreased breath sounds at left lung base. Bronchoscopy showed narrowed left lower lobe bronchus due to the external compression. Computed tomography angiography revealed multiple bilateral pulmonary artery aneurysms. Pathergy test was positive and he was diagnosed with BD. BD should be considered in the differential diagnosis of childhood hemoptysis.
白塞病（BD）是一种罕见的自身免疫性慢性炎症性血管炎，其特征为复发性口腔溃疡、生殖器溃疡、皮肤病变、眼部病变和血管受累。白塞病累及肺动脉较为罕见，但死亡率很高。在本文中，我们报告了一名15岁男性患者，有两个月咯血、咳嗽、发热和体重减轻的病史。体格检查时，听诊发现左肺底部呼吸音减弱。支气管镜检查显示左下叶支气管因外部压迫而狭窄。计算机断层扫描血管造影显示双侧多发肺动脉瘤。针刺反应试验呈阳性，他被诊断为白塞病。儿童咯血的鉴别诊断应考虑白塞病。
