Spindel Jeffrey, Heckroth Matthew, Marsano Luis
Internal Medicine, University of Louisville, Louisville, Kentucky, USA
Internal Medicine, University of Louisville, Louisville, Kentucky, USA.
BMJ Case Rep. 2020 Sep 15;13(9):e235777. doi: 10.1136/bcr-2020-235777.
Autoimmune encephalitis is a rare spectrum of disease that can be a complication of chronic immunosuppression. Diagnosis often requires the presence of antineuronal antibodies, but many causative antibodies have not yet been identified. Antibody-negative autoimmune encephalitis (AbNAE) is especially difficult to diagnose and must rely largely on exclusion of other causes. In chronically immune-suppressed transplant recipients, the differential is broad, likely resulting in underdiagnosis and worse outcomes. Here, we present a 58-year-old liver transplant recipient taking tacrolimus for prevention of chronic rejection who presented with 5 days of confusion, lethargy and lightheadedness. He was diagnosed with AbNAE after an extensive workup and recovered fully after high-dose corticosteroids. Our case highlights the importance of recognising the association between chronic immunosuppression and autoimmune encephalitis. Autoimmune encephalitis, even in the absence of characterised antibodies, should be considered when transplant recipients present with central neurologic symptoms.
自身免疫性脑炎是一种罕见的疾病谱,可能是慢性免疫抑制的并发症。诊断通常需要存在抗神经元抗体,但许多致病抗体尚未被识别。抗体阴性自身免疫性脑炎(AbNAE)尤其难以诊断,很大程度上必须依靠排除其他病因。在长期免疫抑制的移植受者中,鉴别诊断范围广泛,可能导致诊断不足和更差的预后。在此,我们报告一名58岁的肝移植受者,他正在服用他克莫司预防慢性排斥反应,出现了5天的意识模糊、嗜睡和头晕症状。经过全面检查后,他被诊断为AbNAE,在接受大剂量皮质类固醇治疗后完全康复。我们的病例强调了认识慢性免疫抑制与自身免疫性脑炎之间关联的重要性。当移植受者出现中枢神经系统症状时,即使没有特征性抗体,也应考虑自身免疫性脑炎。