Tabrizi Ali, Afshar Ahmadreza, Mohebbi Iraj, Pourjabali Masoumeh, Taleb Hassan
Department of Orthopedics, Imam Khomeini Hospital, Urmia University of Medical Sciences, Urmia, Iran.
Department of Occupational Health, Clinical Research Development Unit of Imam Khomeini Hospital, Urmia University of Medical Sciences, Urmia, Iran.
Surg J (N Y). 2020 Sep 10;6(3):e139-e144. doi: 10.1055/s-0040-1712536. eCollection 2020 Jul.
Schwannomas and neurofibromas are rare benign tumors originating from the peripheral nerve sheath. Tumors in neurofibromatosis are mostly neurofibromas and often appear in the soft tissue of peripheral nerves. In this report, a patient presented with two large adjacent soft tissue tumors in the right wrist and distal forearm which originated from a common nerve. A schwannoma had formed beside a neurofibroma from the ulnar nerve and induced numbness and paresthesia in the little and ring fingers. Although the patient had café au lait spots on the skin, neurofibromatosis was not suspected due to lack of symptoms. The patient was referred to the current research clinic suffering from two soft tissue masses in the wrist and ulnar nerve dysfunction. In neurofibromatosis patients, two tumors of a different nature originating from a common nerve close together have rarely been described in the literature. The patient was treated by en bloc excision of the mass while protecting the nerve fascicles. The follow-up results indicated no neurological symptoms and complete restoration of ulnar nerve function.
施万细胞瘤和神经纤维瘤是起源于周围神经鞘的罕见良性肿瘤。神经纤维瘤病中的肿瘤大多是神经纤维瘤,常出现在周围神经的软组织中。在本报告中,一名患者右腕和前臂远端出现两个相邻的大软组织肿瘤,它们起源于同一根神经。尺神经的神经纤维瘤旁形成了一个施万细胞瘤,导致小指和环指麻木及感觉异常。尽管患者皮肤上有牛奶咖啡斑,但由于没有症状,未怀疑患有神经纤维瘤病。该患者因手腕处有两个软组织肿块及尺神经功能障碍被转诊至当前的研究诊所。在神经纤维瘤病患者中,文献中很少描述起源于同一根神经且位置相邻的两种不同性质的肿瘤。患者接受了肿物整块切除,同时保护神经束。随访结果显示无神经症状,尺神经功能完全恢复。