Nishioka Kazuki, Tsutsumi Satoshi, Teramoto Shinichiro, Nonaka Senshu, Okura Hidehiro, Suzuki Takamoto, Izumi Hiroshi, Ishii Hisato
Department of Neurological Surgery, Juntendo University Urayasu Hospital, 2-1-1 Tomioka, Urayasu, Chiba 279-0021, Japan.
Department of Pathology, Juntendo University Urayasu Hospital, 2-1-1 Tomioka, Urayasu, Chiba 279-0021, Japan.
Radiol Case Rep. 2020 Sep 3;15(11):2129-2135. doi: 10.1016/j.radcr.2020.08.038. eCollection 2020 Nov.
Meningeal hemangiopericytoma (HPC) is an infrequent but distinct entity affecting the craniospinal axis. A previously healthy 48-year-old man sustained a gradually progressing motor weakness in the left lower extremity. CT showed a hyperdense mass in the right frontal lobe. On MRI, it was 29 × 30 × 36 mm in dimension, appeared isointense on T1 and hyperintense on T2, and was intensely enhanced with erosive changes in the inner table adjacent to the tumor. The patient underwent tumor resection. Reflection of the bone flap revealed a punched-out erosion in the inner table with a defect of the dura over the upper part of the tumor. Microscopic findings were consistent with grade III HPC with dural invasion. A punched-out calvarial erosion and dural defect caused by an extra-axial tumor may be a high-grade HPC that requires extensive surgical resection.
脑膜血管外皮细胞瘤(HPC)是一种累及颅脊柱轴的罕见但独特的实体瘤。一名既往健康的48岁男性出现左下肢逐渐进展的运动无力。CT显示右额叶有一个高密度肿块。在MRI上,其大小为29×30×36mm,T1加权像呈等信号,T2加权像呈高信号,并伴有与肿瘤相邻的内板侵蚀性改变的明显强化。患者接受了肿瘤切除术。骨瓣翻开显示内板有一个圆形侵蚀,肿瘤上方硬脑膜有缺损。显微镜检查结果与伴有硬脑膜侵犯的III级HPC一致。由轴外肿瘤引起的颅骨圆形侵蚀和硬脑膜缺损可能是一种高级别HPC,需要广泛的手术切除。