Department of Neurology and Institute of Neurology of First Affiliated Hospital, Institute of Neuroscience, Fujian Key Laboratory of Molecular Neurology, Fujian Medical University, Fuzhou 350005, China.
Department of Neurology and Institute of Neurology of First Affiliated Hospital, Institute of Neuroscience, Fujian Key Laboratory of Molecular Neurology, Fujian Medical University, Fuzhou 350005, China.
J Neuroimmunol. 2020 Nov 15;348:577378. doi: 10.1016/j.jneuroim.2020.577378. Epub 2020 Aug 27.
Type1 autoimmune pancreatitis (AIP) is the first recognized and the most common manifestation of IgG4-related disease. However, AIP patient presented with neuropathy in the extremities have not been reported previously. We reported a rare combination of autoimmune pancreatitis and peripheral neuropathy on an IgG4-related disease patient based on histological features to expand the clinical spectrum of IgG4-related disease.
1 型自身免疫性胰腺炎(AIP)是 IgG4 相关疾病中最早被认识到的也是最常见的表现形式。然而,以前尚未有报道过以四肢周围神经病为表现的 AIP 患者。我们根据组织学特征报道了一例 IgG4 相关疾病患者的自身免疫性胰腺炎和周围神经病的罕见组合,以扩展 IgG4 相关疾病的临床谱。