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肠道淀粉样变性所致吸收不良综合征作为肾细胞癌的表现

Malabsorption Syndrome due to Intestinal Amyloidosis as Presentation of Renal Cell Carcinoma.

作者信息

Bessa Filipe, Gaspar Pedro, Antunes Meireles Pedro, Parreira Maria Inês, Serrazina Pedro Juliana, Teixeira da Silva Marisa, Meneses João, Victorino Rui, Mota Catarina

机构信息

Clínica Universitária de Medicina II, CHLN-Hospital de Santa Maria, Lisbon, Portugal.

出版信息

Case Rep Gastrointest Med. 2020 Sep 5;2020:8854620. doi: 10.1155/2020/8854620. eCollection 2020.

Abstract

Renal cell carcinoma accounts for approximately 3% of adult malignancies. Designated in the literature as "the great masquerader," the great diversity of clinical manifestations is associated with the several paraneoplastic syndromes that potentially accompany it. Paraneoplastic amyloidosis is described in about 3-8% of cases, only exceptionally as an initial manifestation, with uncommon gastrointestinal involvement. A rare case of malabsorption by intestinal amyloidosis is presented as initial manifestation of renal cell carcinoma, emphasizing the need for early recognition of these paraneoplastic conditions.

摘要

肾细胞癌约占成人恶性肿瘤的3%。在文献中它被称为“伪装大师”,其临床表现的多样性与可能伴随的几种副肿瘤综合征有关。副肿瘤性淀粉样变性在约3%-8%的病例中被描述,仅在极少数情况下作为初始表现,胃肠道受累罕见。本文报告一例罕见的以肠道淀粉样变性导致吸收不良为肾细胞癌初始表现的病例,强调了早期识别这些副肿瘤性疾病的必要性。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/478d/7492959/fb681344d0fe/CRIGM2020-8854620.001.jpg

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