Bakr Lubna, Al-Jadaan Mohammad, Younes Mohammad
Department of Cardiac Surgery, Faculty of Medicine, Damascus University, Damascus, Syria.
J Cardiothorac Surg. 2020 Oct 2;15(1):297. doi: 10.1186/s13019-020-01349-y.
While the aneurysms of the membranous septum (AVS) are rare, the possibility that they lead to obstruction is even rarer. To the best of our knowledge, 11 similar cases have been reported since 1982.
Initially, the five-year-old boy was evaluated for dyspnoea that had been present since birth. He did not receive any medical treatment until the previous year. At the age of four, the transthoracic echocardiography showed a large aneurysm extending to the right ventricular outflow tract (RVOT) and causing RVOT stenosis. Complete surgical resection of the aneurysmal tissue was performed, and the boy was discharged home in satisfactory condition.
As the occurrence of RVOT obstruction by a membranous ventricular septal aneurysm is very rare, we are reporting the second case in which an aneurysm of the membranous septum dynamically obstructed the RVOT in a child. We are also reviewing all the previously reported similar cases in the literature. Further studies are needed to obtain a more comprehensive understanding of aneurysms of the membranous septum (AVS).
虽然膜周部室间隔瘤（AVS）较为罕见，但导致梗阻的可能性更为罕见。据我们所知，自1982年以来已报告了11例类似病例。
起初，该5岁男孩因自出生以来就存在的呼吸困难接受评估。直到前一年他都未接受任何治疗。4岁时，经胸超声心动图显示一个大的瘤体延伸至右心室流出道（RVOT）并导致RVOT狭窄。对瘤体组织进行了完整的手术切除，该男孩出院时状况良好。
由于膜周部室间隔瘤导致RVOT梗阻的情况非常罕见，我们在此报告第二例膜周部室间隔瘤动态梗阻儿童RVOT的病例。我们还对文献中所有先前报道的类似病例进行了回顾。需要进一步研究以更全面地了解膜周部室间隔瘤（AVS）。
