Razzouk Louai, Applebaum Robert M, Okamura Charles, Saric Muhamed
Leon H. Charney Division of Cardiology, New York University Langone Medical Center, New York, New York.
Echocardiography. 2013 Sep;30(8):E243-8. doi: 10.1111/echo.12279. Epub 2013 Jul 1.
Anomalies of the membranous portion of the interventricular septum include perimembranous ventricular septal defect and/or membranous septal aneurysm (MSA). In congenitally corrected transposition of the great arteries (L-TGA in sinus solitus), the combination of ventricular inversion and arterial transposition creates a unique anatomic substrate that fosters subpulmonic left ventricular outflow tract obstruction by an MSA. The combination of an L-TGA with subpulmonic obstruction by an MSA is referred to as the windsock syndrome. We report a case of windsock syndrome in a 25-year-old man which is to our knowledge the first three-dimensional echocardiographic description of this congenital entity.
室间隔膜部异常包括膜周部室间隔缺损和/或膜部间隔瘤（MSA）。在先天性矫正型大动脉转位（窦性心律下的L-TGA）中，心室反位和动脉转位的组合形成了一种独特的解剖结构，易导致由MSA引起的肺下左心室流出道梗阻。L-TGA与由MSA引起的肺下梗阻相结合被称为风袋综合征。我们报告了一例25岁男性的风袋综合征病例，据我们所知，这是该先天性疾病的首次三维超声心动图描述。
