Bekdemir Şükran, Gündüz Ahmet Kaan, Ataoğlu Ömür
Ophthalmology Clinic, Polatlı Duatepe State Hospital, Ankara, Turkey.
Department of Ophthalmology, Ankara University Faculty of Medicine, Ankara, Turkey.
Case Rep Ophthalmol Med. 2020 Sep 18;2020:2845035. doi: 10.1155/2020/2845035. eCollection 2020.
A 22-year-old woman presented with progressive swelling of the nasal conjunctiva in the left eye. Anterior segment examination revealed a diffuse cystic appearance to the inferonasal bulbar conjunctiva and plica semilunaris. Anterior segment swept-source optical coherence tomography (OCT) revealed clear hyporeflective spaces demarcated by hyperreflective septae in the affected conjunctiva, consistent with the diagnosis of lymphatic malformation (LM). Magnetic resonance imaging revealed a well circumscribed intraconal mass located inferonasally in the left orbit. Systemic examination revealed a lesion similar to LM on the left hard palate. The left conjunctival mass was excised subtotally. Subsequently, a transconjunctival anterior orbitotomy was performed and the left orbital mass was completely removed intact. Histopathologically, the conjunctival mass was diagnosed as LM and the orbital mass as venous malformation (VM). This case represents a rare coexistence of histopathologically proven conjunctival LM and orbital VM as well as a presumed LM of the hard palate, all 3 lesions occurring in the ipsilateral midface area.
一名22岁女性因左眼鼻侧结膜进行性肿胀就诊。眼前节检查发现鼻下球结膜和半月皱襞呈弥漫性囊肿样外观。眼前节扫频光学相干断层扫描（OCT）显示，患侧结膜内有清晰的低反射间隙，由高反射间隔分隔，符合淋巴管畸形（LM）的诊断。磁共振成像显示左眼眶鼻下象限有一个边界清晰的眶内肿块。全身检查发现左侧硬腭有一个类似LM的病变。左侧结膜肿物大部分切除。随后，进行了经结膜前路眶切开术，完整切除了左侧眼眶肿物。组织病理学检查显示，结膜肿物诊断为LM，眼眶肿物诊断为静脉畸形（VM）。该病例代表了经组织病理学证实的结膜LM、眼眶VM以及推测的硬腭LM罕见地共存，所有3个病变均发生在同侧中面部区域。
