Yamada Shodai, Yagi Kenji, Hirano Kazuhiro, Uno Masaaki
Department of Neurosurgery, Kawasaki Medical School, Kurashiki.
Department of Neurosurgery, Okayama Central Hospital, Okayama, Japan.
Surg Neurol Int. 2020 Sep 12;11:282. doi: 10.25259/SNI_212_2020. eCollection 2020.
In patients with secondary empty sella syndrome (ESS), optic nerve herniation into the sella turcica is caused by shrinkage of the mass lesion at the sella turcica, resulting in visual disturbance. ESS is often surgically treated using chiasmapexy. Here, we report the first case of spontaneous improvement in a patient with ESS.
A 69-year-old woman presented with a month-long history of visual disturbance in the right eye, poor visual acuity, and quadrantanopia in her upper temporal visual field. Magnetic resonance (MR) imaging showed herniation of her right optic nerve and gyrus rectus into the sella turcica. The visual disturbance gradually improved, and the patient's vision became almost normal after a month without any treatment. On repeated MR imaging, it was observed that the herniation of the right optic nerve and gyrus rectus disappeared due to an intrasellar cyst re-expansion. The secondary ESS caused by the shrinkage of the intrasellar cyst resulted in the visual disturbance and re-expansion of the cyst resulted in spontaneous improvement of symptoms. The visual disturbance did not recur for a year.
Patients with secondary ESS without severe symptoms may be followed up conservatively. However, surgical treatment should be applied if symptoms deteriorate or do not improve.
在继发性空蝶鞍综合征(ESS)患者中,视神经疝入蝶鞍是由蝶鞍处占位性病变缩小引起的,从而导致视力障碍。ESS通常采用视交叉固定术进行手术治疗。在此,我们报告首例ESS患者自发改善的病例。
一名69岁女性,右眼视力障碍长达1个月,视力差,颞上象限视野出现象限性偏盲。磁共振成像显示右侧视神经和直回疝入蝶鞍。视力障碍逐渐改善,未经任何治疗1个月后患者视力几乎恢复正常。再次进行磁共振成像检查时,发现右侧视神经和直回的疝入因鞍内囊肿重新扩张而消失。鞍内囊肿缩小导致继发性ESS,引起视力障碍,而囊肿重新扩张导致症状自发改善。视力障碍1年内未复发。
对于无严重症状的继发性ESS患者,可进行保守随访。然而,如果症状恶化或无改善,则应采取手术治疗。