Dermatomyositis is a condition that combines an inflammatory myopathy with characteristic cutaneous disease. This disorder is closely related to polymyositis, which has all the muscular features of dermatomyositits without the presence of skin disease. Both dermatomyositits and polymyositis may occur in the presence of other collagen vascular diseases such as lupus erythematosus, scleroderma, Sjögren's syndrome, rheumatoid arthritis, and various vasculitides. Dermatomyositis seems to be characterized by an increased frequency of internal malignancy and both dermatomyositis and polymyositis are associated with morbidity and mortality. Therefore, prompt and aggressive therapy is necessary.
皮肌炎是一种将炎性肌病与特征性皮肤病相结合的病症。这种疾病与多发性肌炎密切相关,多发性肌炎具有皮肌炎的所有肌肉特征,但不存在皮肤疾病。皮肌炎和多发性肌炎都可能在其他胶原血管疾病如红斑狼疮、硬皮病、干燥综合征、类风湿关节炎和各种血管炎的情况下发生。皮肌炎的特征似乎是内部恶性肿瘤的发生率增加,并且皮肌炎和多发性肌炎都与发病率和死亡率相关。因此,需要迅速而积极的治疗。