Department of Cardiothoracic Surgery, Stanford University Medical Center, Falk Building, 300 Pasteur Dr., Stanford, CA, 94305, USA.
Department of Anesthesiology, Stanford University, Stanford, CA, USA.
Gen Thorac Cardiovasc Surg. 2021 Mar;69(3):555-559. doi: 10.1007/s11748-020-01503-2. Epub 2020 Oct 19.
Intracardiac paragangliomas most commonly arise from the left atrium and are often infiltrative and densely adherent to surrounding structures. Given their rarity, only scattered reports exist in the literature and standardized perioperative and surgical management is not well established. We describe a case of a 60-year-old woman with a mildly functioning intracardiac paraganglioma in which division of the superior vena cava improved exposure and enabled a complex limited resection. Further, we provide an overview of the diagnostic workup, perioperative medical management, surgical approach, and surveillance strategy in patients with these challenging tumors.
心脏内副神经节瘤最常起源于左心房,常呈浸润性生长,与周围结构紧密粘连。由于其罕见性,文献中仅有零星报道,围手术期和手术管理尚无标准化。我们描述了一例 60 岁女性患有轻度功能性心脏内副神经节瘤,其中上腔静脉的分隔改善了显露,从而能够进行复杂的局限性切除术。此外,我们还概述了这些具有挑战性的肿瘤患者的诊断检查、围手术期医学管理、手术入路和监测策略。