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先天性内耳畸形的影像学检查——一种算法方法

Imaging in congenital inner ear malformations-An algorithmic approach.

作者信息

Bhagat Abhinav C, Kumar Jyoti, Garg Anju, Prakash Anjali, Meher Ravi, Arya Shivali

机构信息

Department of Radiodiagnosis, Maulana Azad Medical College and Lok Nayak Hospital, New Delhi, India.

Department of ENT, Maulana Azad Medical College and Lok Nayak Hospital, New Delhi, India.

出版信息

Indian J Radiol Imaging. 2020 Apr-Jun;30(2):139-148. doi: 10.4103/ijri.IJRI_58_19. Epub 2020 Jul 13.

DOI:10.4103/ijri.IJRI_58_19
PMID:33100680
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC7546298/
Abstract

Malformations of the inner ear are an important cause of congenital deaf-mutism. Arrest in embryologic development of inner ear during various stages gives rise to the variety of malformations encountered. Current treatment options include hearing aids, cochlear implants, and auditory brainstem implants (ABI). With the advent of cochlear implant surgery and ABI, decent functional outcomes can be obtained provided such cases are diagnosed correctly and timely. To that end, high-resolution computed tomography (HRCT) has a fundamental role in the assessment of these conditions, ably supplemented by magnetic resonance imaging (MRI). The purpose of this pictorial essay is to illustrate the imaging features of inner ear anomalies in children with congenital deaf-mutism as per the latest terminology and classification and provide an algorithmic approach for their diagnosis.

摘要

内耳畸形是先天性聋哑的一个重要原因。内耳在胚胎发育的各个阶段发生停滞会导致出现各种不同的畸形。目前的治疗选择包括助听器、人工耳蜗植入和听觉脑干植入（ABI）。随着人工耳蜗植入手术和ABI的出现，只要这些病例得到正确及时的诊断，就可以获得较好的功能结果。为此，高分辨率计算机断层扫描（HRCT）在这些病症的评估中具有重要作用，磁共振成像（MRI）可对其进行有效补充。这篇图文并茂的文章旨在根据最新的术语和分类阐述先天性聋哑儿童内耳异常的影像学特征，并提供一种诊断的算法方法。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/31b3/7546298/9a3d250b9ab9/IJRI-30-139-g020.jpg
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J Otol. 2015 Mar;10(1):13-17. doi: 10.1016/j.joto.2015.07.004. Epub 2015 Aug 22.
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Balkan Med J. 2017 Sep 29;34(5):397-411. doi: 10.4274/balkanmedj.2017.0367. Epub 2017 Aug 25.
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Duplicated internal auditory canal with inner ear malformation: Case report and literature review.
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