Department of Cardiology, All India Institute of Medical Sciences, New Delhi, India.
Echocardiography. 2020 Dec;37(12):2168-2170. doi: 10.1111/echo.14914. Epub 2020 Oct 27.
In cor triatriatum sinister, the left atrium is divided by a membrane into a proximal and a distal chamber. Usually proximal chamber receives all the pulmonary veins and drains through an opening in the dividing membrane into distal chamber, which empties into left ventricle through the mitral valve. Rarely, the two chambers lack a communication and there is associated total anomalous pulmonary venous connection (TAPVC). We report a 1-month-old infant with cyanosis and heart failure, who had cor triatriatum sinister associated with supracardiac TAPVC. The case is reported for rarity of the association with a focus on contrast echocardiographic imaging.
在左心房间隔三房心畸形中,左心房被一层隔膜分为近端和远端两个腔室。通常情况下,近端腔室接收所有的肺静脉,并通过隔膜上的开口排入远端腔室,然后通过二尖瓣排入左心室。很少见的情况下,两个腔室之间没有交通,并且存在完全性肺静脉异常连接(TAPVC)。我们报告了一例 1 个月大的婴儿,表现为发绀和心力衰竭,患有左心房间隔三房心畸形合并心上型 TAPVC。该病例罕见,我们重点介绍了对比超声心动图成像。