Devision of Orthopaedics and Traumatology, Department of Orthopaedics, Nanfang Hospital, Southern Medical University, Guangzhou, China.
Department of Health Management, Nanfang Hospital, Southern Medical University, Guangzhou, China.
Haemophilia. 2020 Nov;26(6):e308-e314. doi: 10.1111/hae.14148. Epub 2020 Nov 3.
The incidence of a pelvic haemophilic pseudotumour is very low and is rarely seen in the clinic. Due to the lack of clear treatment standards, patients often suffer from the condition over a protracted period. The aim of this retrospective study was to present our institutional experience in the treatment of pelvic haemophilic pseudotumours over the past 8 years.
We retrospectively analysed patients with a pelvic haemophilic pseudotumour who were treated in the Nanfang hospital between February 2012 and December 2019. The type and severity of haemophilia, the presence of inhibitors, comorbidities, pseudotumour imaging data, treatment and follow-up results were recorded and analysed.
Pelvic pseudotumours were identified in seven patients with haemophilia. Three patients had severe haemophilia, three had moderate haemophilia, one had mild haemophilia and inhibitors were present in two patients. Transfusion-related infectious diseases were noted in three patients. Spontaneous rupture and infection of the pseudotumour occurred in five patients. In addition, five patients underwent surgical treatment, two of whom healed well, two patients suffered recurrence of the pseudotumour, and one patient developed a postoperative haematoma twice. Two patients were treated conservatively, one of whom was unable to walk because of progression of the disease, while the other died from severe bleeding and infection.
Once a pelvic haemophilic pseudotumour is diagnosed, surgical resection should be performed as soon as possible. A delay in diagnosis and suboptimal treatment may lead to complications of the pelvic haemophilic pseudotumour.
骨盆血友病性假瘤的发病率非常低,临床上很少见。由于缺乏明确的治疗标准,患者往往长期患病。本回顾性研究旨在介绍我们机构过去 8 年治疗骨盆血友病性假瘤的经验。
我们回顾性分析了 2012 年 2 月至 2019 年 12 月在南方医院治疗的骨盆血友病性假瘤患者。记录并分析血友病的类型和严重程度、抑制剂的存在、合并症、假瘤影像学数据、治疗和随访结果。
7 例血友病患者发现骨盆假瘤。3 例为重型血友病,3 例为中型血友病,1 例为轻型血友病,2 例存在抑制剂。3 例患者发生与输血相关的传染病。5 例患者的假瘤自发性破裂并感染。此外,5 例患者接受了手术治疗,其中 2 例愈合良好,2 例假瘤复发,1 例术后血肿 2 次。2 例患者接受保守治疗,其中 1 例因疾病进展无法行走,另 1 例因严重出血和感染死亡。
一旦诊断出骨盆血友病性假瘤,应尽快进行手术切除。诊断延迟和治疗不当可能导致骨盆血友病性假瘤的并发症。