Hampton K K, Grant P J, Johnston D, Prentice C R
Department of Medicine, General Infirmary, Leeds, UK.
Blood Coagul Fibrinolysis. 1990 Dec;1(6):747-8.
Haemophilic pseudotumour is a rare but well-recognized complication of moderate and severe haemophilia, particularly in patients who have developed a factor VIII inhibitor. It has only been reported in haemophiliacs with factor VIII or IX levels less than 5%. We report a patient with mild haemophilia (factor VIII 11%, factor IX 78%) who developed a pelvic pseudotumour that was successfully treated with a novel surgical technique and who has no evidence of recurrence five years after operation.
血友病性假肿瘤是中度和重度血友病一种罕见但已被充分认识的并发症,尤其在已产生VIII因子抑制物的患者中。仅在VIII因子或IX因子水平低于5%的血友病患者中有相关报道。我们报告了一名轻度血友病患者(VIII因子11%,IX因子78%),其出现了盆腔假肿瘤,采用一种新型手术技术成功治疗,术后五年无复发迹象。