Singh Saraj Kumar, Kumar Niraj
Department of Neurosurgery, AIIMS, Patna, Bihar, India.
Department of Neurology, AIIMS Rishikesh, Uttarakhand, India.
Asian J Neurosurg. 2020 Aug 28;15(3):695-698. doi: 10.4103/ajns.AJNS_120_20. eCollection 2020 Jul-Sep.
Medulloblastoma (MB) is very rare malignant primary brain tumor in adults and its location at cerebellopontine angle (CPA) is even rarer. There are only few case reports of CPA MBs in literature. Most of them are reported in pediatric age groups which are mostly intraaxial. Only 11 cases of extra-axial CPA MBs have been reported so far. The author is reporting a very rare case of adult extra-axial CPA MBs with multiple intracranial metastases. We are also reviewing clinical and radiological features and unusual way of its presentation along with surgical management. Keeping MBs as one of the differential diagnosis for extra-axial CPA tumors is going to increase our spectrum of diagnosis which can lead to alteration in management.
髓母细胞瘤（MB）是成人中非常罕见的原发性恶性脑肿瘤，其位于桥小脑角（CPA）的情况更为罕见。文献中仅有少数关于CPA区髓母细胞瘤的病例报告。其中大多数报告的是儿童年龄组，且大多为脑内型。迄今为止，仅报告了11例脑外型CPA区髓母细胞瘤。本文作者报告了1例非常罕见的成年脑外型CPA区髓母细胞瘤伴多发颅内转移的病例。我们还回顾了其临床和影像学特征、不寻常的表现方式以及手术治疗情况。将髓母细胞瘤作为脑外型CPA区肿瘤的鉴别诊断之一，将拓宽我们的诊断范围，从而可能改变治疗方案。
