Institute for Brain Research and Rehabilitation, South China Normal University, Guangzhou, China.
Department of Neurology, Guangdong 999 Brain Hospital, Guangzhou, China.
Cerebellum. 2021 Apr;20(2):246-253. doi: 10.1007/s12311-020-01209-4. Epub 2020 Nov 9.
The aim of this study is to evaluate the prevalence and electrophysiological features of 3-Hz postural tremor in multiple system atrophy-cerebellar type and spinocerebellar ataxia. A static posturography examination was administered to 37 persons with spinocerebellar ataxia, 58 others with the cerebellar type of multiple system atrophy, and 53 healthy controls. During the sensory organization tests of 5 multiple system atrophy patients, surface electromyograms were recorded from bilateral tibialis anterior and medial gastrocnemius muscles. The patients with multiple system atrophy had, on average, significantly higher scores on the International Cooperative Ataxia Rating Scale and significantly greater prevalence of cross sign. Almost 80% of them fell during the posturography testing compared with two-thirds of the spinocerebellar ataxia patients. Twenty-seven percent of the spinocerebellar ataxia patients and 82.8% of those with multiple system atrophy displayed postural tremor with a frequency of approximately 3 Hz. The tremor's frequency tended to be lower in the spinocerebellar ataxia patients. The surface electromyography revealed highly coherent tremor activity at about 3 Hz in the patients' bilateral tibialis anterior and alternating firing in the bilateral antagonist muscles. Combining cross sign with a subject's static score of the International Cooperative Ataxia Rating Scale and occurrence of the tremor produced an indicator able to differentiate the two conditions with a sensitivity of 87.9% and a specificity of 89.2%. The area under the receiver operating characteristics curve for the indicator was 0.942. Three-hertz postural tremor is relatively characteristic of cerebellar type of multiple system atrophy and appears at an early stage of the disease. Identification of the tremor by posturography will facilitate its diagnosis.
本研究旨在评估 3-Hz 姿势性震颤在多系统萎缩-小脑型和脊髓小脑共济失调中的患病率和电生理特征。对 37 名脊髓小脑共济失调患者、58 名多系统萎缩小脑型患者和 53 名健康对照者进行静态姿势描记检查。在 5 名多系统萎缩患者的感觉组织测试中,记录双侧胫骨前肌和内侧腓肠肌的表面肌电图。多系统萎缩患者的国际合作共济失调评分平均得分显著较高,交叉征的患病率显著较高。与三分之二的脊髓小脑共济失调患者相比,他们在姿势描记测试中平均有近 80%的人摔倒。27%的脊髓小脑共济失调患者和 82.8%的多系统萎缩患者表现出约 3 Hz 的姿势性震颤。震颤的频率在脊髓小脑共济失调患者中倾向于较低。表面肌电图显示患者双侧胫骨前肌的高度相干震颤活动,频率约为 3 Hz,双侧拮抗肌交替放电。将交叉征与患者国际合作共济失调评分的静态评分和震颤的发生相结合,产生了一种能够以 87.9%的敏感性和 89.2%的特异性区分两种情况的指标。该指标的受试者工作特征曲线下面积为 0.942。3-Hz 姿势性震颤是多系统萎缩小脑型的相对特征性表现,并且在疾病的早期出现。通过姿势描记术识别震颤将有助于其诊断。