Gurbuz Hande, Saracoglu Kemal Tolga
University of Health Sciences, Derince Training and Research Hospital, Department of Anesthesiology and Reanimation, Kocaeli, Turquia.
University of Health Sciences, Kartal Lutfi Kirdar Training and Research Hospital, Department of Anesthesiology and Reanimation, Istanbul, Turquia.
Braz J Anesthesiol. 2020 Nov-Dec;70(6):682-685. doi: 10.1016/j.bjan.2020.07.004. Epub 2020 Oct 14.
Myotonic dystrophy type-1 (Steinert disease) is an autosomal dominant, progressive multisystem disease in which myotonic crisis can be triggered by several factors including pain, emotional stress, hypothermia, shivering, and mechanical or electrical stimulation. In this report, dexmedetomidine-based general anesthesia, in combination with a thoracic epidural for laparoscopic cholecystectomy in a patient with Steinert disease, is presented. An Aintree intubation catheter with the guidance of a fiberoptic bronchoscope was used for intubation to avoid laryngoscopy. Prolonged anesthetic effects of propofol were reversed, and recovery from anesthesia was accelerated using an intravenous infusion of theophylline.
1型强直性肌营养不良症（斯坦纳特病）是一种常染色体显性进行性多系统疾病，其中，肌强直危象可由多种因素引发，包括疼痛、情绪应激、体温过低、寒战以及机械或电刺激。本报告介绍了在一名斯坦纳特病患者行腹腔镜胆囊切除术时，采用右美托咪定全身麻醉联合胸段硬膜外麻醉的情况。在纤维支气管镜引导下使用安特里插管导管进行插管，以避免喉镜检查。使用静脉输注茶碱逆转了丙泊酚的延长麻醉作用，并加速了麻醉苏醒。
