General Hospital of Komotini, Komotini, Greece.
Folia Med (Plovdiv). 2022 Apr 30;64(2):333-336. doi: 10.3897/folmed.64.e59905.
Myotonic dystrophy type 1 or Steinert's disease is an autosomal dominant multisystem disease which is characterized by consistent contracture of muscle following stimulation (myotonia). Hypothermia, shivering, mechanical or electric stimulation during surgery can precipitate episodes of myotonia which may complicate the course of anaesthesia. The present case report focuses on successful strategies for providing general anaesthesia for laparoscopic cholecystectomy in a patient affected by this genetic disorder, at a hospital which does not have the facility for postoperative ventilation.
1 型肌强直性营养不良又称 Steinert 病，是一种常染色体显性多系统疾病，其特征是肌肉在受到刺激后持续收缩（肌强直）。低温、寒战、手术期间的机械或电刺激可诱发肌强直发作，这可能会使麻醉过程复杂化。本病例报告重点介绍了在一家没有术后通气设备的医院，为患有这种遗传性疾病的患者实施腹腔镜胆囊切除术时提供全身麻醉的成功策略。
