Department of Neurological Surgery, Carolinas Medical Center, Charlotte, USA.
Carolina Neurosurgery and Spine Associates, Charlotte, North Carolina, USA.
World Neurosurg. 2021 Feb;146:163-165. doi: 10.1016/j.wneu.2020.11.070. Epub 2020 Nov 18.
An adult with Sprengel deformity and Klippel-Feil syndrome associated with an omovertebral bone has rarely been reported in literature. The omovertebral bone is an abnormal cartilaginous connection between the scapula and the cervical spine. Limited cases have previously been reported in the literature describing surgical intervention when neurologic deficits such as cervical myelopathy or radiculopathy are present. In the present case, an omovertebral bone extended into the cervical lamina resulting in cervical myeloradiculopathy requiring resection of the bony anomaly and cervicothoracic fusion. The omovertebral bone as an etiology for radiculopathy or myelopathy is rarely seen in an adult population, and surgical decompression and fusion should be considered with this constellation of anomalies.
成人 Sprengel 畸形和 Klippel-Feil 综合征伴蝶枕骨连接极为罕见，文献中鲜有报道。蝶枕骨连接是一种肩胛骨和颈椎之间异常的软骨连接。先前的文献中仅有限的病例报告了在存在神经功能缺损如颈椎病或神经根病时进行手术干预。在本病例中，蝶枕骨连接延伸至颈椎椎板，导致颈脊髓神经根病，需要切除骨异常并进行颈椎胸椎融合。在成年人群中，蝶枕骨连接作为神经根病或颈椎病的病因很少见，对于这种畸形的组合，应考虑进行减压和融合手术。
