From the Department of Neurosurgery, King Fahad Hospital, Hofuf, Al-Ahasa, Kingdom of Saudi Arabia.
Neurosciences (Riyadh). 2021 Jan;26(1):89-92. doi: 10.17712/nsj.2021.1.20200040.
Sprengel deformity is a congenital anomaly arising mainly in the shoulder girdle, associated with elevation of dysplastic scapula. skeletal anomalies, mainly Klippel-Feil syndrome, hemivertebrae, and omovertebral bone may be present along Sprengel anomaly. The omovertebral bone is an abnormal bone that originates from the superomedial edge of the scapula with different insertion points along the posterior cervical spine, seen in about third of the patients with Sprengel anomaly. While cosmetic to functional impairment is a common presentation to the omovertebral bone, cervical myelopathy is a rare presentation. Here, we described our experience, management and follow up of 13-year-old boy presented with cervical myelopathy secondary to the omovertebral bone.
Sprengel 畸形是一种主要发生在肩带的先天性异常,与发育不良的肩胛骨抬高有关。骨骼异常,主要是 Klippel-Feil 综合征、半椎体和胸骨骨,可能与 Sprengel 异常同时存在。胸骨骨是一种异常骨,起源于肩胛骨的上内侧缘,沿着颈椎的后背部有不同的插入点,在大约三分之一的 Sprengel 畸形患者中可见。虽然胸骨骨常见的表现为美容到功能受损,但颈椎脊髓病是一种罕见的表现。在这里,我们描述了我们对 13 岁男孩的经验、管理和随访,该男孩因胸骨骨继发颈椎脊髓病。