Department of Radiology Pontificia Universidade Catolica do Rio Grande do Sul Porto Alegre Brazil.
Cardiovascular Division Department of Medicine University of Pennsylvania Philadelphia PA.
J Am Heart Assoc. 2020 Dec;9(23):e018866. doi: 10.1161/JAHA.120.018866. Epub 2020 Nov 21.
Arrhythmogenic right ventricular cardiomyopathy was first described as a right ventricular disease that is an important cause of death in young adults. However, with the advent of advanced imaging, arrhythmogenic right ventricular cardiomyopathy has been found to commonly have biventricular involvement, and a small portion of patients have left ventricular-dominant forms. On the other hand, a number of primarily left ventricular disease such as sarcoid and myocarditis can be arrhythmogenic and have right ventricular involvement. A few recent publications on arrhythmogenic right ventricular cardiomyopathy cohorts have average left ventricular functions that are comparable to sarcoid or myocarditis cohorts. We review the current literature and compare these cohorts of patients, and call for left ventricular functional criteria for arrhythmogenic right ventricular cardiomyopathy as inherited arrhythmogenic cardiomyopathy.
致心律失常性右室心肌病最初被描述为一种右心室疾病，是年轻人死亡的重要原因。然而，随着先进成像技术的出现，致心律失常性右室心肌病通常表现为双心室受累，一小部分患者为左室优势型。另一方面，一些主要的左心室疾病，如结节病和心肌炎，也可能导致心律失常并伴有右心室受累。最近有一些关于致心律失常性右室心肌病患者队列的出版物显示，其平均左心室功能与结节病或心肌炎患者队列相当。我们回顾了目前的文献，并对这些患者队列进行了比较，呼吁将左心室功能标准纳入致心律失常性右室心肌病作为遗传性心律失常性心肌病。
