Department of Radiation Oncology, AIIMS Rishikesh, Rishikesh, Uttarakhand, India.
Department of Radiation Oncology, AIIMS Rishikesh, Rishikesh, Uttarakhand, India
BMJ Case Rep. 2020 Nov 23;13(11):e237678. doi: 10.1136/bcr-2020-237678.
Primary synovial sarcoma of the lung (PSSL) is a rare tumour with only 0.5% incidence among other primary malignant lung tumours. Published medical literature regarding the natural history treatment protocol and clinical outcomes of PSSL remains limited. Here, we present a case of a 39-year-old man with primary synovial sarcoma with long-term follow-up, which was initially viewed as a metastasis from another unknown site. After evaluating histopathologically from the specimen post left lung metastasectomy and ruling out any other site for neoplastic changes, the diagnosis of PSSL was confirmed. Furthermore, this article reviews the literature and discusses various aspects of PSSL, including clinical presentation, radiological imaging and pathological characteristics, diagnostic dilemma, management and prognosis. This paper serves to provide an update and aims to enhance the understanding of PSSL. Timely diagnosis and treatment are imperative to achieve improved outcomes.
肺原发性滑膜肉瘤（PSSL）是一种罕见的肿瘤，在其他原发性肺部恶性肿瘤中的发病率仅为 0.5%。关于 PSSL 的自然病史、治疗方案和临床结果的已发表医学文献仍然有限。在这里，我们报告了一例 39 岁男性的原发性滑膜肉瘤，对其进行了长期随访，最初认为其是来自另一个未知部位的转移。对左肺转移瘤切除术后的标本进行组织病理学评估并排除任何其他部位的肿瘤性改变后，确诊为 PSSL。此外，本文还回顾了文献，并讨论了 PSSL 的各个方面，包括临床表现、影像学和病理学特征、诊断难题、治疗和预后。本文旨在提供最新信息，旨在提高对 PSSL 的认识。及时的诊断和治疗对于改善预后至关重要。
