George Kimberley, Morren Marie-Anne, Christen Thierry, Letovanec Igor, Christen-Zaech Stephanie
Pediatric Dermatology Unit, Departments of Dermatology & Venereology and Pediatrics, University Hospital Lausanne, University of Lausanne, Lausanne, Switzerland.
Hand Plastic Surgery Unit, University Hospital Lausanne, University of Lausanne, Lausanne, Switzerland.
Pediatr Dermatol. 2021 Jan;38(1):187-190. doi: 10.1111/pde.14352. Epub 2020 Nov 27.
Epithelioid sarcoma is a rare soft-tissue tumor that occurs mainly in children and young adults. It typically presents as a subcutaneous or deep dermal mass in distal extremities. Due to its benign-appearing clinical presentation, infrequent occurrence, and histologic similarities with other pathologies, the diagnosis of epithelioid sarcoma in its early stages can be extremely difficult and can be easily confused with benign lesions such as warts or foreign body granuloma. In this paper, we report the case of a 12-year-old boy with a distal-type epithelioid sarcoma of the hand and wish to emphasize the difficulties of diagnosing this potentially lethal tumor both clinically and histologically.
上皮样肉瘤是一种罕见的软组织肿瘤，主要发生于儿童和青年。它通常表现为远端肢体的皮下或真皮深层肿块。由于其临床表现看似良性、发病率低且在组织学上与其他病理情况相似，上皮样肉瘤在早期阶段的诊断极其困难，很容易与良性病变如疣或异物肉芽肿相混淆。在本文中，我们报告了一名12岁手部远端型上皮样肉瘤男孩的病例，并希望强调在临床和组织学上诊断这种潜在致命肿瘤的困难。
