From the Department of Radiodiagnosis, Sher i Kashmir Institute of Medical Sciences, Srinagar, Jammu and Kashmir, India.
From the Department of Pediatric Cardiology, GB Panth Children's Hospital, Srinagar, Jammu and Kashmir, India.
Ann Saudi Med. 2020 Nov-Dec;40(6):496-500. doi: 10.5144/0256-4947.2020.496. Epub 2020 Dec 3.
Double-chambered right ventricles (DCRV) and left ventricles are rare entities on their own. We present two cases with an unusual combination of double-chambered right as well as left ventricles. One was discovered in a 28-year-old female, while the other was found at birth in a female child. The differing nature of both the patient demographics as well as the presentation with a common morphological background is shown on both computed tomography and magnetic resonance imaging. The oldest description of an obstructive muscular band within the right ventricle was given in 1867. In the literature, there is ample description of the long-term prognosis and management guidelines for DCRV, but no inheritance patterns or risk factors have been identified except for associations with septal defects, tetralogy of Fallot and transposition of the great arteries. A combination of both double-sided left as well as right ventricles has been published in literature a few times with little details about management and prognosis. SIMILAR CASES PUBLISHED: Although many cases of DCRV and DCLV have been published, to our knowledge only 3 cases of combined DCRV and DCLV have been published in literature.
双腔右心室(DCRV)和左心室本身就是罕见的实体。我们提出了两个具有双腔右心室和左心室异常组合的病例。一个在 28 岁女性中发现,另一个在一名女性婴儿中出生时发现。这两个病例的患者特征和临床表现都不同,这在计算机断层扫描和磁共振成像上都有显示。1867 年首次描述了右心室的阻塞性肌带。文献中对 DCRV 的长期预后和管理指南有充分的描述,但除了与间隔缺损、法洛四联症和大动脉转位有关外,尚未确定遗传模式或危险因素。双侧左心室和右心室的组合在文献中也有几次报道,但关于管理和预后的细节很少。类似病例发表:尽管已经发表了许多 DCRV 和 DCLV 的病例,但据我们所知,文献中仅报道了 3 例 DCRV 和 DCLV 的合并病例。